  Case reportAnomalous origin of the left coronary artery from the pulmonary artery (ALCAPA) presenting with ventricular fibrillation in an adult: a case reportThomas Kristensen1  , Klaus Fuglsang Kofoed2  , Steffen Helqvist2 , Morten Helvind2 and Lars Søndergaard2 1Department of Radiology, Diagnostic Centre, Rigshospitalet, University of Copenhagen, Denmark 2Department of Cardiology and Thoracic Surgery, The Heart Centre, Rigshospitalet, University of Copenhagen, Denmark  author email corresponding author email
Journal of Cardiothoracic Surgery 2008,
3:33doi:10.1186/1749-8090-3-33 Abstract
Anomalous origin of the left coronary artery from the pulmonary artery (ALCAPA) is a rare congenital anomaly. The usual clinical course is severe left sided heart failure and mitral valve insufficiency presenting during the first months of life. However, in some cases collateral blood supply from the right coronary artery is sufficient and symptoms may be subtle or even absent. Arrhythmias or sudden cardiac death in adult life may be the first clinical presentation in patients with ALCAPA. We report a case, where a 39-year old woman presented with ventricular fibrillation during phycial exertion. Coronary angiography and CT-angiography revealed an anomalous origin of the left coronary artery, and an aortic reimplantation of the left coronary artery was performed followed by ICD implantation. A review of the literature on ALCAPA is presented along with CT images before and after surgery. | 
on Google Scholar
