Progressive cyanosis following Kawashima operation: slow resolution after redirection of hepatic veins
1 Department of Cardiology, Aarhus University Hospital, Brendstrupgaardsvej, 8200 Aarhus N, Denmark
2 Department of Pediatrics, Aarhus University Hospital, Brendstrupgaardsvej, 8200 Aarhus N, Denmark
3 Department of Cardiothoracic surgery, Aarhus University Hospital, Brendstrupgaardsvej, 8200 Aarhus N, Denmark
Journal of Cardiothoracic Surgery 2013, 8:67 doi:10.1186/1749-8090-8-67Published: 5 April 2013
Progressive cyanosis often develops following Kawashima operation in patients with left atrial isomerism, interrupted inferior vena cava and hepatic veins draining to the atria. Knowledge on the timing and extend of resolution following hepatic venous redirection is sparse. A girl developed progressing cyanosis following Kawashima operation at the age of ten months. Arterial oxygen saturations at rest dropped to 60-65%. Surgical redirection of hepatic veins into the cavopulmonary circulation at the age of three years had no immediate effect. However, arterial oxygen saturations increased gradually over nine months to 90-93% and 95-100% after three years.